Exam 33: Neurological and Neuromuscular Disorders

Which of the following forms of poliomyelitis affects the nerves in the cervical spine region that control diaphragmatic function?

Which of the following measurements is the main determinant of respiratory compromise in pediatric patients with neuromuscular disease?

Which of the following muscles is considered a primary muscle of inspiration?

Which of the following diagnostic evaluations is/are appropriate for children with neuromuscular dysfunction who exhibit progressive carbon dioxide retention, increasing muscle weakness, and advancing concerns regarding nighttime hypoventilation?

Which of the following therapeutic strategies should the therapist deem as the most important in patients with neuromuscular disease?

The therapist is performing an airway clearance technique to a 5-month-old child with a diagnosis of aspiration pneumonia. The child has a very weak cough and, although he appears alert, he cannot move. Which of the following disorders of the motor nerve should the therapist suspect?

The therapist is asked to evaluate a young child with a diagnosis of Chiari malformation. Which of the following signs and symptoms should the therapist expect to see? I. Irregular breathing II. Difficulty swallowing III. Vomiting IV. Choking

Which of the following diseases is characterized by chronic, slowly progressive muscle wasting and weakness, cataracts, heart conduction defects, and endocrine disorders?

What are the goals of assisted ventilation in children with progressive neuromuscular disease? I. Maintain pulmonary compliance II. Maintain normal alveolar ventilation III. Slow the disease progression IV. Prevent muscle weakness from developing

Which of the following glycogen storage diseases has the most severe respiratory symptoms?

What are the names of the separate pathways in the spinal cord that support both voluntary and involuntary ventilation and transmit signals through descending pathways to motor neurons?

What are the consequences of bulbar muscle dysfunction? I. Dysphagia II. Impaired coughing III. Dysarthria IV. Impaired inspiration

Which of the following neuromuscular diseases is characterized in early childhood by progressive muscle weakness, followed by skeletal and respiratory muscle weakness, and in adolescence by confinement to a wheelchair and requirement for ventilatory assistance?

A therapist is administering incentive spirometry to a patient who demonstrates ptosis, diplopia, and a weak cough. The patient has a history of a minimal chronic respiratory disease. Which of the following disorders is likely affecting this patient?

Ondine's curse, or congenital central hypoventilation syndrome, occurs during which activity?

Which of the following diseases is characterized by demyelination of sheaths that coat peripheral nerves?