Exam 15: Cystic Fibrosis

Common chest assessment findings in a patient with cystic fibrosis include: 1) tracheal deviation. 2) breath sounds reveal crackles and rhonchi. 3) dull percussion note. 4) hyperresonant percussion note.

Which of the following are considered classifications of CFTR mutations? 1) Gating defect 2) Conductance defect 3) Sol layer defect 4) Periciliary defect

Cystic fibrosis patients can have: 1) malnutrition. 2) a meconium ileus (bowel obstruction). 3) excessive, viscous pulmonary secretions. 4) a tendency for status asthmaticus.

Which of the following are recommended in children with cystic fibrosis? 1) Systemic corticosteroids 2) High-dose ibuprofen 3) Inhaled antibiotics 4) Inhaled DNase (Dornase alpha) (Pulmozyme)

Cystic fibrosis is a gene disorder caused by mutations in a pair of genes located on chromosome ______.

What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis?

Which of the following chest assessment findings may be seen in a patient with cystic fibrosis? 1) Decreased tactile and vocal fremitus 2) Dull percussion note 3) Diminished breath sounds 4) Decreased heart sounds

If both the mother and the father are carriers for the cystic fibrosis gene, what are the chances that their child will be a cystic fibrosis carrier?

Which of the following are commonly used in the management of cystic fibrosis? 1) Pancreatic enzymes and vitamins 2) Antibiotics 3) Postural drainage 4) Antitussives

Which ethnic group has the greatest number of people with cystic fibrosis?

During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have:

Which of the following are commonly cultured from the mucus in the tracheobronchial tree of a patient with cystic fibrosis? 1) Klebsiella 2) Pseudomonas aeruginosa 3) Haemophilus influenzae 4) Staphylococcus aureus

Which of the following may be recommended to reduce bronchial inflammation in a 10-year-old child with cystic fibrosis?

A patient has a lung infection with Pseudomonas aeruginosa. What antibiotic should be used against it?

The major pathologic or structural changes associated with cystic fibrosis include: 1) partial airway obstruction leading to hyperinflation. 2) bronchospasm. 3) thick, tenacious mucus. 4) total airway obstruction leading to atelectasis.

A cystic fibrosis patient in generally good condition may be a candidate for which of the following?

Which of the following can be used in the diagnosis of cystic fibrosis? 1) An elevated potassium level in the sweat 2) An elevated chloride level in the sweat 3) Genetic testing of the parents 4) An elevated blood level of immunoreactive trypsin

How can the genetic mutation found with cystic fibrosis (CF) be characterized? 1) There are many variations in the mutation. 2) CF is the most common fatal childhood inherited disorder. 3) The mutation is a dominant trait. 4) The mutation stops ciliary function.

Which of the following pulmonary function findings would be expected in a patient with moderate to severe cystic fibrosis? 1) Increased FVC 2) Increased RV 3) Decreased PEFR 4) Decreased FEF_50%

Men with cystic fibrosis have difficulty reproducing because the: