Question 1

What are the three phases of autogenic drainage

Accepted Answer

A)  Unstick, Collect, and evacuate
B)  Hold, expectorate, and examine
C)  Breath hold, mobilize, and expectorate
D)  Mobilize, expectorate, and empty A

Question 2

What pulmonary function test marker(s) best Correlate with instances of mortality in patients with cystic fibrosis
I.Forced vital capacity
II.Forced expiratory volume after 1 seCond divided by forced expiratory volume after 6 seConds
III.Functional residual capacity
IV.Forced expiratory volume after 1 seCond

Accepted Answer

A)  I and III
B)  II and IV
C)  IV only
D)  I and IV D

Question 3

Which of the following practices facilitate muCous clearance in patients with cystic fibrosis
I.Positive expiratory pressure therapy
II.Low-frequency inspiratory oscillation
III.Positive end-expiratory pressure therapy
IV.High-frequency expiratory oscillation

Accepted Answer

A)  II and III
B)  I and II
C)  III and IV
D)  I and IV D

Question 4

Which of the following are Contraindications to lung transplantation for patients with cystic fibrosis
I.Poor adherence to therapy
II.Normal body mass index
III.UnControlled diabetes
IV.Colonization with resistant organisms

Accepted Answer

A)  I and IV
B)  I, II, and III
C)  I, III, and IV
D)  I, II, III, and IV

Question 5

What information should be Considered when creating an individualized treatment plan for a patient with cystic fibrosis
I.Age
II.Gender
III.Symptoms
IV.Pulmonary function test results
V.Severity of lung disease

Accepted Answer

A)  II, IV, and V
B)  I, II, and III
C)  I, II, III, and V
D)  I, III, and V

Question 6

Which of the following are muColytic agents
I.Dornase alfa
II.Pulmozyme
III.Hypotonic saline solutions
IV.Tobramycin
V.Acetylcysteine

Accepted Answer

A)  I and V
B)  I, II, and V
C)  II, III, and IV
D)  I, II, III, IV, and V

Question 7

What is Considered the most Common life-shortening genetic disease among Caucasians

Accepted Answer

A)  Bronchiectasis
B)  Cystic fibrosis
C)  Down syndrome
D)  Sickle-cell disease

Question 8

What was the median survival age for patients with cystic fibrosis as of 2010

Accepted Answer

A)  27.2
B)  30.6
C)  35.4
D)  38.3

Question 9

What percentage of adults with cystic fibrosis (CF) develop CF-related diabetes

Accepted Answer

A)  10%
B)  25%
C)  33%
D)  50%

Question 10

Which of the following techniques are not Considered when managing a patient with cystic fibrosis
I.Airway clearance technique
II.Bronchial hygiene therapy
III.Hig- frequency chest wall oscillation
IV.Total chest breathing technique
V.High-pressure positive expiratory pressure therapy
VI.Drainage autogenic dyssynchrony
VII.Intrapulmonary percussive ventilation
VIII.Aerosol therapy and muColytic therapy

Accepted Answer

A)  II, III, IV, and VIII
B)  I, V, and VI
C)  IV, and VII
D)  I, II, and IV

Question 11

What are some symptoms that Could signify the presence of cystic fibrosis
I.Difficulty gaining weight
II.Abnormal stools
III.Potassium deficiency
IV.CT scan revealing bronchiectasis and muCous plugging

Accepted Answer

A)  I, II, and III
B)  I, II, and IV
C)  I, III, and IV
D)  II, III, and IV

Question 12

What is the standardized order for delivery of inhaled medications and airway clearance

Accepted Answer

A)  Bronchodilator, hypertonic saline, airway clearance, dornase alfa, inhaled antibiotics, and inhaled steroids
B)  Bronchodilator, hypertonic saline, dornase alfa, airway clearance, inhaled steroids, and inhaled antibiotics
C)  Bronchodilator, airway clearance, dornase alfa, hypertonic saline, inhaled steroids, and inhaled antibiotics
D)  Bronchodilator, dornase alfa, hypertonic saline, airway clearance, inhaled antibiotics, and inhaled steroids

Question 13

What role does exercise play in improving lung function for patients with cystic fibrosis
I.Increase minute ventilation
II.Decrease minute ventilation
III.Decrease expiratory flow
IV.Increase expiratory flow

Accepted Answer

A)  II and IV
B)  I and III
C)  I and IV
D)  II and III

Question 14

What factors hasten the progression of lung disease in patients with cystic fibrosis
I.Infection with Pseudomonas aeruginosa
II.Infection with Burkholderia cenocepacia
III.Male patient
IV.Diabetes
V.Exposure to seCondhand smoke

Accepted Answer

A)  I, IV, and V
B)  II, III, and IV
C)  II, IV, and V
D)  I, III, and V

Question 15

What is the reCognized testing standard for diagnosing cystic fibrosis
I.Sweat test
II.Pilocarpine iontophoresis
III.Cystic fibrosis transmembrane Conductance regulator gene sequencing
IV.Nasal potential difference

Accepted Answer

A)  I and II
B)  II and IV
C)  II and III
D)  I and III

Question 16

What is the most Common bacterium found in the airways of patients with cystic fibrosis

Accepted Answer

A)  StaphyloCoccus aureus
B)  Pseudomonas aeruginosa
C)  Burkholderia cenocepacia
D)  Methicillin-resistant StaphyloCoccus aureus

Question 17

What is the only FDA-approved nebulizer for use with inhaled tobramycin

Accepted Answer

A)  Sidestream nebulizer
B)  PARI LC PLUS nebulizer
C)  TRIO nebulizer
D)  Altera nebulizer

Question 18

Which of the following inhaled antibiotics are approved to treat a patient with cystic fibrosis
I.Tobramycin
II.Aztreonam
III.Pulmozyme
IV.Colistin

Accepted Answer

A)  I, II, and IV
B)  I and III
C)  I and IV
D)  I only

Question 19

What percentage of patients with cystic fibrosis present with bowel obstructions

Accepted Answer

A)  20%-25%
B)  30%-35%
C)  10%-15%
D)  25%-30%

Question 20

What action should be performed to stop transmission of pathogens from one cystic fibrosis patient to another

Accepted Answer

A)  Disinfecting equipment by cleaning with vinegar solution
B)  Autoclave sterilization of equipment
C)  Hand washing
D)  Distillation process

Exam 14: Pediatric Disease With Respiratory Implications

What are the three phases of autogenic drainage

Which of the following practices facilitate muCous clearance in patients with cystic fibrosis I.Positive expiratory pressure therapy II.Low-frequency inspiratory oscillation III.Positive end-expiratory pressure therapy IV.High-frequency expiratory oscillation

Which of the following are Contraindications to lung transplantation for patients with cystic fibrosis I.Poor adherence to therapy II.Normal body mass index III.UnControlled diabetes IV.Colonization with resistant organisms

What information should be Considered when creating an individualized treatment plan for a patient with cystic fibrosis I.Age II.Gender III.Symptoms IV.Pulmonary function test results V.Severity of lung disease

Which of the following are muColytic agents I.Dornase alfa II.Pulmozyme III.Hypotonic saline solutions IV.Tobramycin V.Acetylcysteine

What is Considered the most Common life-shortening genetic disease among Caucasians

What was the median survival age for patients with cystic fibrosis as of 2010

What percentage of adults with cystic fibrosis (CF) develop CF-related diabetes

What are some symptoms that Could signify the presence of cystic fibrosis I.Difficulty gaining weight II.Abnormal stools III.Potassium deficiency IV.CT scan revealing bronchiectasis and muCous plugging

What is the standardized order for delivery of inhaled medications and airway clearance

What role does exercise play in improving lung function for patients with cystic fibrosis I.Increase minute ventilation II.Decrease minute ventilation III.Decrease expiratory flow IV.Increase expiratory flow

What factors hasten the progression of lung disease in patients with cystic fibrosis I.Infection with Pseudomonas aeruginosa II.Infection with Burkholderia cenocepacia III.Male patient IV.Diabetes V.Exposure to seCondhand smoke

What is the reCognized testing standard for diagnosing cystic fibrosis I.Sweat test II.Pilocarpine iontophoresis III.Cystic fibrosis transmembrane Conductance regulator gene sequencing IV.Nasal potential difference

What is the most Common bacterium found in the airways of patients with cystic fibrosis

What is the only FDA-approved nebulizer for use with inhaled tobramycin

Which of the following inhaled antibiotics are approved to treat a patient with cystic fibrosis I.Tobramycin II.Aztreonam III.Pulmozyme IV.Colistin

What percentage of patients with cystic fibrosis present with bowel obstructions

What action should be performed to stop transmission of pathogens from one cystic fibrosis patient to another